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Otosclerosis

Otosclerosis is one of the most common causes of progressive deafness in young adults.

Otosclerosis is an abnormal growth of bone in the ears. In most cases, a surgical operation will restore normal hearing.

The disease has to do with the three small bones in the middle ear, more specifically the stapes. A part of the bone will grow abnormally. The bone growth will prevent the stapes from vibrating normally in response to sound. At this early stage, the person will not be affected.

Otosclerosis is often inherited, although isolated cases do occur. Both ears may be affected but it is more common for one ear to be more severely affected than the other. If left untreated, hearing loss typically worsens progressively until late middle age when complete deafness occurs.

The most famous otosclerosis victim is said to have been Beethoven. Deafness made him unable to hear his late compositions.
Symptoms
The diagnosis should be made by specialists, but some signs can be detected by the suffering person himself or his relatives.

Strong background noise usually adds to the confusion of people with nerve deafness, but in the case of otosclerosis, this confusion does not often occur. Sometimes, the person may even hear better in noisy surroundings, possibly because of the high frequency and loudness of other people's voices in those circumstances. Otosclerosis tends to affect low frequencies more than high ones.
What to do
Hearing aids help people who are suffering from conductive deafness, including otosclerosis. However, a hearing aid will not cure the deafness. Since the deafness is progressive, more powerful hearing aids may be needed as time goes. At the early stages, hearing aids are a great help for those who do not wish to undergo surgery.

A straightforward surgical operation is now widely performed, and it is a relatively simple procedure. The operation can restore normal hearing in most cases.

Diseases:
 Otosclerosis
 Glue Ear
 Loudness Discomfort
 Hyperacusis
 Usher's Syndrome
 Acoustic Trauma
 Patulous Eustachian tube
 Acoustic Tumours
 Ehlers-Danlos Syndrom
 Pendred Syndrome
 Autoimmune Inner Ear Disease
 Labyrinthitis
 Central auditory processing disorders
 Alport syndrome
 Treacher Collins Syndrome
 Stickler Syndrome
More:
 Conductive hearing loss
 Sensorineural hearing loss
 Sudden hearing loss
 Ménière ́s disease
 Otitis Media
 Otitis Externa
 Single sided deafness
Read also:
 Living with hearing loss
 Hearing loss widespread