Ehlers-Danlos Syndrome

What is Ehlers-Danlos Syndrome? Ehlers-Danlos Syndrome is a rare syndrome that can cause a defect in the sound conducting mechanism of the middle ear, and which may result in hearing loss.

Normally when sound waves enter the ear they are conducted from the middle ear to the inner ear by three tiny bone joints called the hammer, the anvil and the stirrup. But due to the syndrome the joints may become hypermobile. This may cause the sound not to be conducted effectively from the middle to the inner ear.

Patients suffering from hearing loss caused by Ehlers-Danlos Syndrome may find that hearing aids are the most effective remedy.

In addition, Ehlers-Danlos Syndrome may cause other symptoms such as skin or heart problems.

Cause of Ehlers-Danlos Syndrome

Basically, Ehlers-Danlos Syndrome is a defect in the connection tissue in the body. The defect is caused by a mutation in the genes which control the formation of albumen (protein) from which the connective tissue is built. The Ehlers-Danlos Syndrome is hereditary.

Get our news about hearing loss

If you want to receive news from us on hearing loss and other hearing related issues, then please subscribe for our newsletter
Can you pass our hearing test?
Try hearing test
Listen to hearing loss
Get news updates from hear-it
How good is your hearing?
Can you pass our hearing test ?
Try free hearing test